Overcoming odds: neonatal survival in absent right main pulmonary artery with unilateral right pulmonary hypoplasia

Abstract

A unilateral absent pulmonary artery with unilateral pulmonary hypoplasia is an exceptionally rare congenital anomaly. This case report details the management of a neonate diagnosed antenatally with absent right main pulmonary artery and right pulmonary hypoplasia. The neonate developed respiratory failure within 24 hours of birth and was successfully managed with invasive ventilation and conservative treatment. Despite episodes of bronchiolitis during infancy, the child demonstrated normal growth and development at 1 year. This case highlights the importance of early diagnosis, multidisciplinary care and vigilant follow-up in achieving favourable outcomes in rare congenital conditions.